ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA - CASE REPORT FROM PAKISTAN AND REVIEW OF LITERATURE
DOI:
https://doi.org/10.47144/phj.v35i1-4.84Keywords:
RIGHT VENTRICULAR DYSPLASIAAbstract
Arrhythmogenic right ventricular dysplasia (ARVD)is disorder of cardiac muscle characterized by the
replacement of myocytes by fibrofatty tissue and
extracellular matrix.ARVD is a genetic cardiomyopathy characterized by
fibrous-adipose substitution of the right (6) and rarely
of the left ventricular myocardium (7).An important focus of
the evaluation of a patient diagnosed with ARVD is to
identify those at risk for SCD.ARVD is a rare disorder with a very
heterogenous presentation. The disease is frequently
asymptomatic until adolescence and the findings on
testing are subtle - hence frequently missed.
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